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Table 1 Laboratory data of the studied Cohort (n = 56)

From: Native kidney and graft survival in a cohort of Egyptian children with nephropathic cystinosis: national referral center experience

Variable

Category

n = 56

Kidney functions

Blood Urea (mg/dl)

Mean ± SD

72.32 ± 66.7

Median (Range)

46 (6 – 250)

Serum Creatinine (mg/dl)

Mean ± SD

2.99 ± 2.7

Median (Range)

1.1 (0.3 – 9.3)

e-GFR

Mean ± SD

37.61 ± 33.1

 

Median (Range)

36 (4 – 120)

Serum Electrolytes

Ca (mg/dl)

Mean ± SD

8.96 ± 1.7

 

Median (Range)

9.6 (5.3 – 11.5)

PO4 (mg/dl)

Mean ± SD

4.20 ± 1.1

 

Median (Range)

4 (2 – 9)

Na (mmol/L)

Mean ± SD

139.01 ± 6.5

 

Median (Range)

139 (130 – 156)

K (mmol/L)

Mean ± SD

3.92 ± 1.1

Median (Range)

3.8 (2 – 6)

CBC

Hgb (g/dl)

Mean ± SD

10.38 ± 2.5

 

Median (Range)

11 (6 – 14)

MCV(fl)

Mean ± SD

79.42 ± 6.2

 

Median (Range)

79.5 (69 – 90)

MCH(pg)

Mean ± SD

26.61 ± 2.1

 

Median (Range)

27 (23 – 29.5)

Hct (%)

Mean ± SD

30.44 ± 6.6

 

Median (Range)

32 (18 – 40)

TLC(10*3/cmm)

Mean ± SD

8.38 ± 3.2

 

Median (Range)

7.5 (2.5 – 14.5)

Platelet(10*3/cmm)

Mean ± SD

309.06 ± 105.2

 

Median (Range)

323 (54 – 532)

Other Parameters

ALP(U/l)

Mean ± SD

462.53 ± 328.9

 

Median (Range)

340 (138 – 1277)

Albumin(g/dl)

Mean ± SD

4.31 ± 0.7

 

Median (Range)

4.5 (2.8 – 5.1)

PH

Mean ± SD

7.36 ± 0.1

 

Median (Range)

7.4 (7.2 – 7.5)

Bicarbonate (mmEq/l)

Mean ± SD

20.91 ± 6.6

 

Median (Range)

21 (10 – 32)

  1. e-GFR Estimated glomerular filtration rate, Ca Calcium, PO4 Phosphorus, Na Sodium, K Potassium, Hbg Haemoglobin, MCV mean corpuscular volume, MCH mean corpuscular haemoglobin, Hct hematocrite, TLC total leukocytic count, ALP alkaline phosphatase